Ebstein
anomaly
The
tricuspid valve is malformed and its wall junction is lower than normal.
Consequently the valve is incompetent and right atrium and ventricle
do not work regularly. 

-Fig. 6.13
Ebstein
anomaly of tricuspid valve. The arro indicates the anomalous inplant
of the tricuspid valve. The tip of arrow indicates the correct position-.
Sometimes
the pressure in right atrium increases until it allows blood to flow
into left atrium through an atrial septal defect generally present.
In this cases the children will be cyanotic, Some forms of Ebstein anomaly
are light and well tolerated. When surgery is necessary generally it
do not require to be performed in pediatric age; it consist in a valvuloplasty
or substitution of the valve with a prosthetic valve.
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