Ebstein anomaly

The tricuspid valve is malformed and its wall junction is lower than normal. Consequently the valve is incompetent and right atrium and ventricle do not work regularly.



-Fig. 6.13
Ebstein anomaly of tricuspid valve. The arro indicates the anomalous inplant of the tricuspid valve. The tip of arrow indicates the correct position-.


Sometimes the pressure in right atrium increases until it allows blood to flow into left atrium through an atrial septal defect generally present. In this cases the children will be cyanotic, Some forms of Ebstein anomaly are light and well tolerated. When surgery is necessary generally it do not require to be performed in pediatric age; it consist in a valvuloplasty or substitution of the valve with a prosthetic valve.

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